Pulmonary Atresia with VSD and PDA

  • This defect is a form of Tetralogy of Fallot in which there is complete obstruction of the Pulmonary Artery resulting in total diversion of blood from the right ventricle into the aorta. Survival depends on the ductus remaining open in the early days of life (in order for blood to reach the lungs), or on the presence of other connecting blood vessels between the Aorta and the Pulmonary Arteries in the lungs (Collaterals).

    Affected infants usually become blue soon after birth (as the ductus closes). Early surgery (a so called 'Shunt' operation) involves insertion of a tiny piece of artificial tube (made from Goretex) between the Aorta, or a branch (usually one of the arm arteries), and one of the branch Pulmonary Arteries (LPA or RPA). Corrective surgery is carried out later in childhood.

    15a_Pulmonary_atresia_with_VSD

     

    Urgent operation is often needed in the newborn period. This is a usually a 'shunt' operation.
    Complete repair is usually postponed until the age of one to three years. Repair usually necessitates the use of a graft valve to replace the missing Pulmonary Valve ('Conduit').

    15b_Pulmonary_atresia_with_VSD