In this section
This defect is a form of Tetralogy of Fallot in which there is
complete obstruction of the Pulmonary Artery resulting in total
diversion of blood from the right ventricle into the aorta.
Survival depends on the ductus remaining open in the early days of
life (in order for blood to reach the lungs), or on the presence of
other connecting blood vessels between the Aorta and the Pulmonary
Arteries in the lungs (Collaterals).
Affected infants usually become blue soon after birth (as the
ductus closes). Early surgery (a so called 'Shunt' operation)
involves insertion of a tiny piece of artificial tube (made from
Goretex) between the Aorta, or a branch (usually one of the arm
arteries), and one of the branch Pulmonary Arteries (LPA or RPA).
Corrective surgery is carried out later in childhood.
Urgent operation is often needed in the newborn period. This is
a usually a 'shunt' operation.
Complete repair is usually postponed until the age of one to three
years. Repair usually necessitates the use of a graft valve to
replace the missing Pulmonary Valve ('Conduit').