In this section
The Aorta arises from the right ventricle and receives "blue"
blood, whilst the Pulmonary Artery arises from the left ventricle
(Transposition). The presence of pulmonary stenosis often protects
the pulmonary circulation from the effects of high pressure
(pulmonary hypertension), while the VSD allows adequate flow of
blood from the left side of the heart into the main circulation
maintain good oxygen levels. Many affected children can survive for
many months or even years (sometimes into adult life) without
surgery. If the pulmonary stenosis is severe then flow of blood in
the lungs may be inadequate and early surgery (e.g. a 'shunt'
operation) may be needed.
Conversely if the pulmonary stenosis is mild then pulmonary
hypertension may be present and surgery may be needed to prevent
this causing damage to the lungs.
Corrective surgery often involves a Rastelli operation. This
results in blood being channelled through the VSD from the
left ventricle to the Aorta. A patch in the right ventricle
prevents blood passing from the RV to the Aorta. A conduit (which
is an artificial tube containing a graft valve) is sewn in to
connect the right ventricle to the Pulmonary Artery. A similar
operation is called the 'REV' procedure.